Urinalysis and Body Fluids 6th Edition by Majorie DiLorenzo, Susan Strasinger

Exercise 27

The classic urine color associated with porphyria is:

A. Dark yellow

B. Indigo blue

C. Pink

D. Port wine

Step 1 of 2

Porphyrinuria:

It is the presence of excess porphyrin in urine also termed as porphyria.

• Porphyrins are intermediate compounds, which help in production of heme

• Disorders in metabolism of porphyrin are collectively called as porphyrias

• Port wine color of urine is observed when exposed to air. It indicates porphyrinuria presence

• Port wine urine color is much prevalent in erythropoietic porphyrias where staining of teeth occurs

• Congenital porphyria is suspected from presence of red discoloration in infant’s diapers

• Screening test for porphyrinuria use florescence test, and Ehrlich reaction

Therefore, the color of urine related with porphyria is “port wine”. Hence, the correct answer is option.